以重度贫血为首要表现的特发性肺含铁血黄素沉着症1例
Journal: Basic Medical Theory Research DOI: 10.12238/bmtr.v7i6.17060
Abstract
特发性肺含铁血黄素沉着症（IPH）是一组肺泡毛细血管出血性疾病，常反复发作，并以大量含铁血黄素积累于肺内为特征[1]，多见于儿童。IPH典型临床三联征缺铁性贫血、咯血、弥漫性肺浸润影。痰、纤维支气管镜肺泡灌洗液或肺活检组织中找到含铁血黄素巨噬细胞是确诊依据，以糖皮质激素为一线治疗药物[2]。该病起病隐匿，症状与体征缺乏特异性，易导致误诊，使疾病延续。现对肇庆市高要区人民医院2025年收治的1例IPH患儿进行病例总结，以增强临床医生尤其是基层医院医生对该病的认识，从而提高临床医生对该病的诊治水平。
Keywords
肺含铁血黄素沉着症；咯血；缺铁性贫血
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